Primary Intrarenal Neuroblastoma with Hypertension and Disseminated Intravascular Coagulation

نویسندگان

  • Bibi Shahin Shamsian
  • Mohammad Kajizadi
  • Nima Rezaei
  • Nozar Ghojehvand
  • Roxana Azma
  • Mohsen Rouzrokh
  • Maryam Kazemi Aghdam
  • Seyed Malek Mesbah
  • Farid Ghazizadeh
  • Mohammad Taghi Arzanian
چکیده

The primary intrarenal neuroblastoma (IRNB) is a rare condition. Intrarenal neuroblastoma typically results from direct renal invasion from an adrenal neuroblastoma, but true intrarenal neuroblastoma originates either sequestered adrenal rests during the fetal life or intrarenal sympathetic ganglia. Clinical, radiological, and pathological correlation is very essential for diagnosis and appropriate management of this type of unusual cases. The distinction of this rare tumor from Wilms' tumor is an important challenge since both tumors have major differences in prognostic and therapeutic response. We present a 3-year-old boy of primary intrarenal neuroblastoma with extensive abdominal and mediastinal mass, persistent hypertension, and disseminated intravascular coagulation (DIC).

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عنوان ژورنال:

دوره 2013  شماره 

صفحات  -

تاریخ انتشار 2013